ornithine transcarbamylase

noun

Medical Definition of ornithine transcarbamylase

: an enzyme of hepatic mitochondria that catalyzes the conversion of ornithine to citrulline as part of urea formation and that when deficient in the body results in hyperammonemia, vomiting, coma, seizures, and sometimes death

called also ornithine carbamoyltransferase, ornithine transcarbamoylase