gangliosidosis

noun
gan·​gli·​o·​si·​do·​sis | \ ˌgaŋ-glē-ˌō-sī-ˈdō-səs How to pronounce gangliosidosis (audio) \
plural gangliosidoses\ -​ˌsēz How to pronounce gangliosidoses (audio) \

Medical Definition of gangliosidosis

: any of several inherited metabolic diseases (as Tay-Sachs disease) characterized by an enzyme deficiency which causes accumulation of gangliosides in the tissues