fucosidosis

noun
fu·​co·​si·​do·​sis | \ -ˌkō-sə-ˈdō-səs How to pronounce fucosidosis (audio) \
plural fucosidoses\ -​ˌsēz How to pronounce fucosidoses (audio) \

Medical Definition of fucosidosis

: a disorder of metabolism inherited as a recessive trait and characterized by progressive neurological degeneration, deficiency of the alpha stereoisomer of fucosidase, and accumulation of fucose-containing carbohydrates